Porphyria
What are the treatments for the disease?
Treatment depends on the type of porphyria. Treatment of acute, or short term, intermittent porphyria includes intravenous fluids and glucose. Other
treatments may include:
strong pain medications for abdominal pain.
hematin, an enzyme inhibitor that can help prevent or treat attacks
tranquilizers to reduce anxiety
medications such as beta-carotene to reduce light sensitivity and the
effects of sunlight
a diet high in carbohydrates
surgery, such as a spleen removal to treat anemia
What are the side effects of the treatments?
Pain medications may cause stomach
upset, irritability, and drowsiness. Surgery poses a risk of
bleeding, infection, and allergic reaction
to anesthesia.
What happens after treatment for the disease?
A person with porphyria may have relapses, in which the condition worsens and symptoms return.
How is the disease monitored?
The person is monitored for relapses. Blood and urine tests may also be used to monitor the levels of porphyrins in the blood and urine. Further treatment will be given when symptoms or attacks occur. Any new or worsening symptoms should be reported to the healthcare provider.
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